铜转运蛋白质β链抗体
产品名称： 铜转运蛋白质β链抗体
英文名称： ATP7B
产品编号： bs-1718R
产品价格： null
产品产地： 北京
品牌商标： BIOSS
更新时间： 2025-01-23T14:13:33
使用范围： WB=1:100-500,ELISA=1:500-1000,IHC-P=1:100-500,IHC-F=1:100-500,Flow-Cyt=1:50-500,IF=1:100-500,
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ATP7b is an important protein for copper transport and elimination of excess copper from the body. ATP7b transports metals in and out of cells using ATP. There are 3 known isoforms of the ATP7b gene; A is found in the liver, kidney, and brain, the shorter form B is found in brain tissue, and the third isoform, known as WND/140 KDA is found in mitochondria. Mutations in the ATP7b gene can cause Wilson's disease, an inherited disorder causing copper poisoning in the brain and liver.